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BCKDHB Proteins

BCKDHB Human recombinant proteins are validated for use in the following applications: Blocking Assay. These proteins are expressed in E. coli. Available Product Grades: RUO. Browse all 2 proteins. Not finding the exact protein, grade or size needed?... BCKDHB Human recombinant proteins are validated for use in the following applications: Blocking Assay. These proteins are expressed in E. coli. Available Product Grades: RUO. Browse all 2 proteins. Not finding the exact protein, grade or size needed? Contact us... BCKDHB Human recombinant proteins are validated for use in the following applications: Blocking Assay. These proteins are expressed in E. coli. Available Product Grades: RUO. Browse all 2 proteins. Not finding the exact protein, grade or size needed? Contact us to discuss your specific application and product needs.... BCKDHB Human recombinant proteins are validated for use in the following applications: Blocking Assay. These proteins are expressed in E. coli. Available Product Grades: RUO. Browse all 2 proteins. Not finding the exact protein, grade or size needed? Contact us to discuss your specific application and product needs.

Protein Information

Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems.

Synonyms

2-oxoisovalerate dehydrogenase beta subunit; 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial; BCKD BCKDH E1-beta; BCKDE1B; BCKDH E1-beta; Bckdhb; branched chain alpha-ketoacid dehydrogenase E1-beta subunit; branched chain keto acid dehydrogenase E1 beta; branched chain keto acid dehydrogenase E1 subunit beta; branched chain keto acid dehydrogenase E1, beta polypeptide; branched chain ketoacid dehydrogenase E1, beta polypeptide; Branched-chain alpha-keto acid dehydrogenase E1 component beta chain; dJ279A18.1; E1B; E1b-beta subunit of the branched-chain complex; testis secretory sperm-binding protein Li 240mP

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Clicking the images or links will redirect you to a website hosted by BenchSci that provides third-party scientific content. Neither the content nor the BenchSci technology and processes for selection have been evaluated by us; we are providing them as-is and without warranty of any kind, including for use or application of the Thermo Fisher Scientific products presented.

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Invitrogen
Human BCKDHB (aa 50-112) Control Fragment Recombinant Protein
Invitrogen
Human BCKDHB (aa 50-112) Control Fragment Recombinant Protein
Host
Species
Human
Expression System
E. coli
Product Grade
Research Use Only
Application
Ctrl BLOCK
Price
Special offer
Online exclusive
Online offer:
Cat # RP-94643

100 µL

Invitrogen
Human BCKDHB (aa 306-386) Control Fragment Recombinant Protein
Invitrogen
Human BCKDHB (aa 306-386) Control Fragment Recombinant Protein
Host
Species
Human
Expression System
E. coli
Product Grade
Research Use Only
Application
Ctrl BLOCK
Price
Special offer
Online exclusive
Online offer:
Cat # RP-108805

100 µL

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